Figure 2From: A neonatal case of 3-hydroxy-3-methylglutaric-coenzyme A lyase deficiency Urinary organic acids profile with evident increasing in 3-hydroxy-isovaleric, 3-methylglutaric, glutaric, 3-methyl-glutaconic, 3-hydroxy-3-methyl-glutaric acids and 3-methyl-crotonyl-glicine. Back to article page