Immunologic aspects of patients with disseminated bacille Calmette-Guerin disease in north-west of Iran

Table 2 summary of data on children with disseminated BCG infection

Number	Age/sex	Site(s) of dissemination	Immune defect	Outcome	Consanguinity	Family history immunodeficiency
1	9 mo/M	Chest, Spleen	MSMD	Survived	-
2	3year/M	As cite, CNS Bone	CGD	died	-
3	4 mo/M	DLN, Liver	SCID Rag₂ deficiency T-B-NK+	died	+	+
4	4 mo/M	Bone, Pericardia Liver	Omen syn T+B-NK+	died	+
5	6 mo/F	Gastric aspirate, DLN	T-B-NK+ SCID	died	-
6	5 mo/F	DLN, Liver	T-B-NK+ SCID	died	+	+
7	4/5 mo/M	Eye, DLN, Lung (Miliary)	*T-B-NK+ SCID	died	+
8	5 mo/F	As cite, Liver, DLN	SCID T-B+NK+	died	+
9	3.5 years/M	Bone, Skin, DLN	MSMD	Survived	-	+
10	4 mo/F	DLN, Gastric aspiration	IL₁₂ R deficiency	Survived	+
11	4 mo/F	Urine, Liver	SCID T-B+NK+	died	+

* Exclusion of Rag₁, Rag₂ and Artemis defect
CMID = cell mediated immune defect, CGD = chronic granulomatous disease, SCID = severe combined immunodeficiency, DLN = distal lymph node.

ISSN: 1824-7288