Table 3 Comparison of patients’ clinical parameters and health-related quality of life scores according to body mass index

Number, (%)

11 (25)

11 (25)

16 (36.4)

6 (13.6)

Age, yr ± SD

12.18 ± 3.09

10.55 ± 2.46

11.81 ± 3.02

13.17 ± 2.79

10.89-12.65

0.32

Shwachman-Kulczycki score ± SD

55.0 ± 11.18

81.82 ± 3.37

82.19 ± 7.52

90.83 ± 9.17

71.89-81.06

0.000

Pseudomonas aeruginosa positive, n (%)

9 (81.8)

4 (36.4)

7 (43.8)

1 (16.7)

0.04

Hospitalised, n (%)

9 (81.8)

4 (50)

2 (14.3)

0 (0)

0.001

FEV₁ ± SD

48.45 ± 18.02

83.27 ± 16.57

89.00 ± 12.91

105.33 ± 14.03

72.23-87.09

0.000

Health-related quality of life (CFQ-R) Patients

Physical functioning ± SD

55.18 ± 29.33

81.25 ± 11.13

80.12 ± 21.38

78.94 ± 18.81

66.56-81.12

0.02

Emotional functioning ± SD

70.08 ± 9.20

76.42 ± 12.41

79.12 ± 12.41

79.17 ± 7.28

72.69-79.67

0.19

Social limitations ± SD

68.11 ± 12.88

73.54 ± 14.85

72.47 ± 16.61

63.23 ± 13.59

65.75-74.88

0.50

Eating disturbances ± SD

68.69 ± 20.98

70.00 ± 32.31

90.97 ± 16.84

90.74 ± 10.92

73.06-87.67

0.02

Treatment burden ± SD

65.66 ± 22.47

70.00 ± 26.22

84.72 ± 12.75

81.48 ± 16.72

69.59-82.34

0.07

Body image ± SD

47.47 ± 28.15

73.33 ± 27.32

80.56 ± 22.77

87.04 ± 14.77

62.74-79.889

0.005

Respiratory symptoms ± SD

53.57 ± 21.27

74.52 ± 16.53

67.83 ± 14.50

79.76 ± 12.39

62.02-73.45

0.01

Digestive symptoms ± SD

90.00 ± 14.29

83.33 ± 22.38

81.95 ± 23.96

83.34 ± 18.26

78.04-90.75

0.80

Health-related quality of life (CFQ-R) Caregivers

Physical functioning ± SD

46.76 ± 33.12

91.20 ± 10.60

87.26 ± 14.07

67.90 ± 2.13

66.96-85.90

0.000

Emotional functioning ± SD

76.67 ± 16.33

84.07 ± 5.72

76.95 ± 18.17

71.11 ± 13.88

73.06-83.61

0.53

Vitality ± SD

66.67 ± 16.33

76.67 ± 14.25

69.99 ± 11.55

60.00 ± 6.67

64.89-74.90

0.27

Eating disturbances ± SD

64.58 ± 31.42

74.07 ± 39.18

79.17 ± 21.47

66.67 ± 0.00

62.59-83.24

0.02

Treatment burden ± SD

44.45 ± 19.70

64.19 ± 14.46

65.74 ± 18.02

70.37 ± 42.07

52.67-68.16

0.10

Body image ± SD

61.11 ± 26.56

76.54 ± 23.20

85.19 ± 19.15

68.52 ± 27.40

66.56-83.79

0.16

Weight ± SD

29.17 ± 37.53

40.74 ± 32.39

86.11 ± 17.16

100.0 ± 0.00

46.62-74.22

0.000

School performance ± SD

66.67 ± 30.86

86.42 ± 17.37

77.77 ± 23.69

85.19 ± 25.66

69.34-86.91

0.39

Health perception ± SD

50.00 ± 31.43

69.14 ± 22.07

70.37 ± 19.73

70.37 ± 16.97

56.23-73.63

0.26

Respiratory symptoms ± SD

58.13 ± 21.81

79.80 ± 18.01

80.89 ± 10.31

79.889 ± 19.14

68.01-81.45

0.03

Digestive symptoms ± SD

75.00 ± 19.47

74.69 ± 13.92

63.89 ± 15.80

70.37 ± 23.13

64.22-76.41

0.42