Skip to main content

Table 1 Vasculitis: classification (Adapted from EULAR/PReS endorsed criteria for the classification of childhood vasculitis) 2006; 65:936-41

From: Vasculitis and Systemic Lupus Erythematous (SLE)

Vasculitis in large calibre vessels prevalence

• Takayasu arteritis

Vasculitis in medium caliber vessels prevalence

• Nodose Polyarteritis

• Cutaneous polyarteritis

• Kawasaki desease

Vasculitis in small calibre vessels

A.Granulomatous

• Wegener Granulomatosis

• Churg-Strauss syndrome

B. Non granulomatous

• Microscopic polyangiitis

• Schönlein-Henoch syndrome

• LVC isolated

• Urticarial vasculitis ipocomplementemica

Other forms

• Behcet desease

• Vasculitis secondary to infection (including nodose polyarteritis associated with hepatitis B), in tumor sand infections, including hypersensitivity vasculitis)

• Connective tissue diseases associated vasculitis

• Isolated SNC vasculitis

• Cogan syndrome

• Not classified vasculitis