Table 2 Cochleo-vestibular malformations as classified by Sennaroglu and Saatci[20]
Malformation | Characteristics |
|---|---|
Labyrinthine aplasia | Complete absence of cochlea and vestibule |
Cochlear aplasia | Cochlea absent, vestibule present |
Common cavity | Cochlea and vestibule are represented by a single, undifferentiated cystic cavity |
Incomplete partition type 1 | Cystic-appearing cochlea lacking entire modiolus and cribriform area; large cystic vestibule |
Cochlear hypoplasia | Cochlea and vestibule smaller than normal |
Incomplete partition type 2 | Cochlea consists of 1.5 turns (normally it has 2.5 turns); middle and apical turns coalesce to form a cystic apex |