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Table 1 Manifestations of cardiac involvement in nemaline myopathy

From: Potential causes of sudden cardiac death in nemaline myopathy

Cardiac abnormality NOP Sex Age (y) Reference
SA-block 1 nm nm [2]
WPW-syndrome 1 nm nm [2]
Atrial fibrillation 1 m 69 [3]
Incomplete BBB 1 m 50 [4]
Complete BBB 1 m 47 [10]
Left anterior hemiblock 1 m 50 [4]
Pulmonary hypertension 1 m 50 [4]
dCMP 6 f, 4 m, nm 9, 26, 29, 47, 50, nm [4, 5, 1113]
hCMP 8 5 m/2 nm 20/0/2/4/5/0/nm [6, 7, 10, 1419]
Outflow tract obstruction 1 nm Neonate [6, 14]
Heart failure 4 f, 2 m, nm 0/9, 3, nm [5, 7, 20]
Sudden cardiac death 2 f 47, 37 [5]
  1. NOP Number of patients, SA Sino-atrial, WPW Wolff-Parkinson-White, BBB Bundle branch block, dCMP Dilated cardiomyopathy, hCMP Hypertrophic cardiomyopathy, nm Not mentioned