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Table 1 CLUFT: Grading system of Abramson et al. [4]

From: Moebius syndrome: clinical features, diagnosis, management and early intervention

CLUFT Clinical Features

Grading

C: Cranial nerves

 

 VII nerve partial

0

 VI nerve partial

1

 VI e VII nerve complete

2

 Additional nerve involvement

3

 If bilateral and equal add

B

L: Lower extremity

 

 Normal

0

 Talipes equinovarus, syndactyly, ankylosis

1

 Absent phalanges

2

 Longitudinal or transverse defect

3

U: Upper extremity

 

 Normal

0

 Digital hypoplasia or failure of differentiation

1

 Ectrodactyly

2

 Failure of longitudinal or transverse formation

3

F: Facial structural anomalies

 

 Normal

0

 Cleft palate

1

 Micrognathia

2

 Microtia, microphtalmia, abnormal joint etc.

3

T: Thorax

 

 Normal

0

 Scoliosis

1

 Pectoral hypoplasia or breast anomaly

2

 Chest wall deformity, breast or pectoral aplasia

3

 Total Score