From: Moebius syndrome: clinical features, diagnosis, management and early intervention
CLUFT Clinical Features | Grading |
---|---|
C: Cranial nerves | |
VII nerve partial | 0 |
VI nerve partial | 1 |
VI e VII nerve complete | 2 |
Additional nerve involvement | 3 |
If bilateral and equal add | B |
L: Lower extremity | |
Normal | 0 |
Talipes equinovarus, syndactyly, ankylosis | 1 |
Absent phalanges | 2 |
Longitudinal or transverse defect | 3 |
U: Upper extremity | |
Normal | 0 |
Digital hypoplasia or failure of differentiation | 1 |
Ectrodactyly | 2 |
Failure of longitudinal or transverse formation | 3 |
F: Facial structural anomalies | |
Normal | 0 |
Cleft palate | 1 |
Micrognathia | 2 |
Microtia, microphtalmia, abnormal joint etc. | 3 |
T: Thorax | |
Normal | 0 |
Scoliosis | 1 |
Pectoral hypoplasia or breast anomaly | 2 |
Chest wall deformity, breast or pectoral aplasia | 3 |
Total Score |