Table 2 Histopathologic features of the lung biopsy

Microscopic analysis

Marked CD138+ plasma cells and lymphocytes

Infiltrations by IgG4-positive plasma cells with IgG4:IgG >40 %

IgG4 cells per HPF >10

Storiform fibrosis

Obliterative vascular lesions (EvG staining)

IHC reactions

Alk 19 (−)

β-catenin (−)

desmin (−)

vimentin (+)

SMA (−)

EMA (+)

WT1 (−)

AFP (−)

Myogenin (−)

MyoD1 (−)

Glipican 1 (−)

CD34 (−)

Other stainings

Trichrom-Masson (+)

Amyloid (−)