From: ANCA-associated vasculitis in childhood: recent advances
I Predominantly large-vessel vasculitis |
• Takayasu arteritis |
II Predominantly medium-sized vessel vasculitis |
• Childhood polyarteritis nodosa • Cutaneous polyarteritis • Kawasaki disease |
III Predominantly small-vessel vasculitis |
(A) GRANULOMATOUS • Wegener’s granulomatosis • Churg-Strauss syndrome (B) NON-GRANULOMATOUS • Microscopic polyangiitis • Henoch-Schönlein purpura • Isolated cutaneous leucocytoclastic vasculitis • Hypocomplementic urticarial vasculitis |
IV Other vasculitides |
• Behçet disease • Vasculitis secondary to infection (including hepatitis B associated polyarteritis nodosa), malignancies, and drugs, including hypersensivity vasculitis • Vasculitis associated with connective tissue diseases • Isolated vasculitis of the central nervous system • Cogan syndrome • Unclassified |