Table 2 Clinical data of the enrolled patients
From: S737F is a new CFTR mutation typical of patients originally from the Tuscany region in Italy
Patient | Age (years) | PS | FEV1 | Sputum pathogens | Pc BMI (°) | SCL at enrolment (mEq/l) | Follow up (years) |
|---|---|---|---|---|---|---|---|
1 | 9,5 | Yes | NA | Hi, Mssa | 95 | 46 | 9,5 |
2 | 8,4 | Yes | 99 | Mssa | >95 | 98 | 6,6 |
3 | 9,7 | Yes | 101 | Hi | 95 | 78 | 9,7 |
4 | 8,8 | Yes | 96 | Mssa, Sm | 75–85 | 94 | 8,8 |
5 | 15,7 | Yes | 99 | Pa | 75–85 | 89 | 14.9 |
6 | 15,8 | Yes | 108 | Mssa | 50–75 | 121 | 15,8 |
7 | 10,7 | Yes | 114 | Mssa | > 95 | 60 | 10,7 |
8 | 0,5 | Yes | NA | Mssa | >95a | 68 | 0,5 |
9 | 1,5 | Yes | NA | Hi | 90a | 67 | 1,5 |