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Fig. 1 | Italian Journal of Pediatrics

Fig. 1

From: Biochemical and molecular analysis in mucopolysaccharidoses: what a paediatrician must know

Fig. 1

Stepwise degradation of the main glycosaminoglycan chains, heparan sulphate (HS), dermatan sulphate (DS), and keratan sulphate (KS). The enzymes involved in the pathway are shown in black. Defective enzyme activity leading to the different types of mucopolysaccharidosis (MPS) is indicated in blue. Note that the degradation pathway of chondroitin sulphates, being similar to that of DS, is not shown

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