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Table 2 Respiratory manifestations in classic/severe forms of MPS disorders

From: ENT and mucopolysaccharidoses

MPS

Upper airway obstruction

Lower airway obstruction

Restrictive lung disease

I

+++

+++

+++

II

+++

+++

++

III

Minimal

Minimal

Minimal

IV

++

+

+++

VI

+++

+++

++

VII

+++

+++

++

  1. Data from Rapoport et al. [40]
  2. MPS mucopolysaccharidosis