Skip to main content

Table 3 Obstructive sleep apnoea (OSA) distribution and severity in each type of MPS

From: ENT and mucopolysaccharidoses

 

No. of patients

MPS type (n)

OSA prevalence

OSA rating

Kiely, 2017 [3]

55

MPS I

32.7%

NA

Gonuldas, 2014 [1]

76

(only 42 studied with polysomnography)

MPS I (8)

MPS II (9)

MPS III (23)

MPS IV (13)

MPS VI (21)

MPS VII (2)

95%

Mild (40.47%)

Moderate (14.28%)

Severe (40.47%)

Morimoto, 2014 [41]

35

MPS I (5)

MPS II (25)

MPS III (2)

MPS IV (2)

MPS VI (1)

43%

NA

Kasapkara, 2014 [42]

19

MPS I (4)

MPS II (4)

MPS VI (11)

94.7%

Mild (26.3%)

Moderate (10.5%)

Severe (57.9%)

Mesolella, 2013 [2]

20

MPS I (7)

MPS II (6)

MPS III (4)

MPS IV (1)

MPS VI (2)

45%

NA

John, 2011 [12]

28

MPS VI

85.1%

Mild (14.28%)

Moderate (17.85%)

Severe (50%)

Lin, 2010 [14]

24

MPS I (3)

MPS II (15)

MPS III (1)

MPS IV (1)

MPS VI (4)

100%

Mild (9.1%)

Moderate (31.81%)

Severe (59.09%)

Nashed, 2009 [15]

11

MPS IH (4)

MPS IH/S (2)

MPS II (3)

MPS IV (2)

64%

Mild (9.09%)

Moderate (27.27%)

Severe (27.27%)

Schwartz, 2007 [43]

120

MPS II

48%

NA

Leighton, 2001 [13]

26

MPS I (10)

MPS II (6)

MPS III (4)

MPS IV (4)

MPS VI (2)

92%

NA

  1. MPS mucopolysaccharidosis, NA not available