| No. of patients | MPS type (n) | OSA prevalence | OSA rating |
---|---|---|---|---|
Kiely, 2017 [3] | 55 | MPS I | 32.7% | NA |
Gonuldas, 2014 [1] | 76 (only 42 studied with polysomnography) | MPS I (8) MPS II (9) MPS III (23) MPS IV (13) MPS VI (21) MPS VII (2) | 95% | Mild (40.47%) Moderate (14.28%) Severe (40.47%) |
Morimoto, 2014 [41] | 35 | MPS I (5) MPS II (25) MPS III (2) MPS IV (2) MPS VI (1) | 43% | NA |
Kasapkara, 2014 [42] | 19 | MPS I (4) MPS II (4) MPS VI (11) | 94.7% | Mild (26.3%) Moderate (10.5%) Severe (57.9%) |
Mesolella, 2013 [2] | 20 | MPS I (7) MPS II (6) MPS III (4) MPS IV (1) MPS VI (2) | 45% | NA |
John, 2011 [12] | 28 | MPS VI | 85.1% | Mild (14.28%) Moderate (17.85%) Severe (50%) |
Lin, 2010 [14] | 24 | MPS I (3) MPS II (15) MPS III (1) MPS IV (1) MPS VI (4) | 100% | Mild (9.1%) Moderate (31.81%) Severe (59.09%) |
Nashed, 2009 [15] | 11 | MPS IH (4) MPS IH/S (2) MPS II (3) MPS IV (2) | 64% | Mild (9.09%) Moderate (27.27%) Severe (27.27%) |
Schwartz, 2007 [43] | 120 | MPS II | 48% | NA |
Leighton, 2001 [13] | 26 | MPS I (10) MPS II (6) MPS III (4) MPS IV (4) MPS VI (2) | 92% | NA |