| No. of patients | MPS type (n) | Surgery (%) |
---|---|---|---|
Cohen, 2017 [34] | 43 | MPS III | T&A (23.25%) |
Kiely, 2017 [3] | 55 | MPS I | A (72.7%) T (61.8%) |
Gonuldas, 2014 [1] | 76 | MPS I (8) MPS II (9) MPS III (23) MPS IV (13) MPS VI (21) MPS VII (2) | T&A (34.21%) |
Kasapkara, 2014 [42] | 19 | MPS I (4) MPS II (4) MPS VI (11) | A (26.3%) T (5.3%) T&A(15.8%) |
Muhlebach, 2013 [37] | 31 | MPS I (9) MPS II (19) MPS III (1) MPS IV (1) MPS VI (1) | T&A (16.12%) |
Mesolell, 2013 [2] | 20 | MPS I (7) MPS II (6) MPS III (4) MPS IV (1) MPS VI (2) | A (15%) T (10%) T&A (25%) |
Malik, 2013 [19] | 10 | MPS II | T&A (70%) |
John, 2011 [12] | 28 | MPS VI | A (21.4%%) T&A (10.7%) |
Mendelsohn, 2010 [7] | 527 | MPS II | A (49.5%) T (35.5%) |
Yeung, 2009 [29] | 27 | MPS IH (8) MPS IH/S (3) MPS II (5) MPS IIIB (1) MPS VI (1) | T&A (70.37%) |