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Table 4 MPS and adenotonsillectomy

From: ENT and mucopolysaccharidoses

 

No. of patients

MPS type (n)

Surgery (%)

Cohen, 2017 [34]

43

MPS III

T&A (23.25%)

Kiely, 2017 [3]

55

MPS I

A (72.7%)

T (61.8%)

Gonuldas, 2014 [1]

76

MPS I (8)

MPS II (9)

MPS III (23)

MPS IV (13)

MPS VI (21)

MPS VII (2)

T&A (34.21%)

Kasapkara, 2014 [42]

19

MPS I (4)

MPS II (4)

MPS VI (11)

A (26.3%)

T (5.3%)

T&A(15.8%)

Muhlebach, 2013 [37]

31

MPS I (9)

MPS II (19)

MPS III (1)

MPS IV (1)

MPS VI (1)

T&A (16.12%)

Mesolell, 2013 [2]

20

MPS I (7)

MPS II (6)

MPS III (4)

MPS IV (1)

MPS VI (2)

A (15%)

T (10%)

T&A (25%)

Malik, 2013 [19]

10

MPS II

T&A (70%)

John, 2011 [12]

28

MPS VI

A (21.4%%)

T&A (10.7%)

Mendelsohn, 2010 [7]

527

MPS II

A (49.5%)

T (35.5%)

Yeung, 2009 [29]

27

MPS IH (8)

MPS IH/S (3)

MPS II (5)

MPS IIIB (1)

MPS VI (1)

T&A (70.37%)

  1. A adenoidectomy, MPS mucopolysaccharidosis, T tonsillectomy, T&A adenotonsillectomy