Table 1 [5, 11,12,13,14,15,16,17,18,19,20,21,22] Summary of the major paediatric case reports (pub med indexed) on hepatic glycogenosis in type 1 diabetes

Franzese (2001)

14 ys/F

11 years

Hepatomegaly, cushingoid appearance, puberty delay, elevation of aminotransferases and triglycerides

Resolution

Carcione (2003)

3 ys/F

1 month

Hepatomegaly, elevation of aminotransferases

Resolution

Mahesh (2007)

3 ys/M

2 years

Hepatomegaly, short stature, elevation of aminotransferases

Resolution

Aljabri (2011)

13 ys/M

3 years

Hepatomegaly, elevation of aminotransferases

Unknown

Dantuluri (2012)

14 ys/F

5 years

Mild hepatomegaly

Unknown

Lin (2012)

10 ys/F

7 years

Hepatomegaly, elevation of aminotransferases

Resolution

Saisuka (2013)

13 ys/F

4 years

Hepatomegaly, elevation of aminotransferases

Unknown

Gutch (2013)

15 ys/M

8 years

Hepatomegaly, short stature, puberty delay, elevation of aminotransferases

Resolution

Oeschgef (2014)

11 ys/F 10 ys/M 14 ys/F 14 ys/F 13 ys/F

2 years 3 years 11 years 8 years 10 years

Hepatomegaly, cushingoid appearance, elevation of aminotransferases and triglycerides Hepatomegaly, short stature, elevation of aminotrasferases Hepatomegaly, short stature, cushingoid appearance, puberty delay, elevation of aminotransferases Hepatomegaly, short stature, cushingoid appearance, puberty delay, elevation of aminotransferases Hepatomegaly, short stature, cushingoid appearance, puberty delay, elevation of aminotransferases

Unknown Resolution Resolution Poor improvement Resolution

Butts (2014)

13 ys/F

2 years

Hepatomegaly, elevation of aminotransferases

Unknown

Chandel (2017)

12 ys/F

5 years

Hepatomegaly, elevation of aminotransferases

Resolution

Al Sarkhy (2017)

6 ys/F

4 years

Hepatomegaly, elevation of aminotransferases

Resolution

Kocova (2018)

13 ys/M

8 years

Hepatomegaly, short stature, cushingoid appearance, puberty delay, elevation of aminotransferases

Resolution