Months of ERT (28 days/month) | Proportion of ventilator time | MRC scale | |||
---|---|---|---|---|---|
Invasive BiPAP% | Invasive CPAP% | NIV% or time | UL | LL | |
0.0 | 100 | 0 | 10 min | 3 | 3+ |
0.5 | 29 | 71 | 0 | 3 | 3+ |
1.0 | 21 | 79 | 30 min | 4 | 3+ |
1.5 | 14 | 86 | 0 | 4+ | 3+ |
2.0 | 0 | 100 | 0 | 5- | 4- |
2.5–3.5 | 20 | 80 | 0 | 5- | 4 |
4.0–5.0 | 0 | 100 | 0 | 5 | 5- |
5.5a | 79 | 21 | 2 h | 5 | 5 |
6.0 | 7 | 93 | 0 | 5 | 5 |
6.5–7.0 | 0 | 100 | 0 | 5 | 5 |
7.5 | 14 | 86 | 2d | 5 | 5 |
8.0–8.5 | 15 | 85 | 0 | 5 | 5 |
9.0 | 64 | 14 | 3d | 5 | 5 |
9.5–10.5 | 6 | 94 | 0 | 5 | 5 |
11.0 | 57 | 0 | 6d | 5 | 5 |
11.5–13.5 | 37 | 63 | 0 | 5 | 5 |
14.0–14.5a | 100 | 0 | 0 | 5 | 5 |
15.0b | 29 | 0 | 0 | 5 | 5 |