Comprehensive approach to weaning in difficult-to-wean infantile and juvenile-onset glycogen-storage disease type II patients: a case series

Table 5 Cardiac structure and function after ERT in children with infantile GSD II

Months of ERT (28 days/month)	Age (months)			Interventricular septal thickness (mm)			Left ventricular ejection fraction(%)
Months of ERT (28 days/month)	P4^a	P5	P6^a	P4^a	P5	P6^a	P4^a	P5	P6^a
0.0	34	3	5	12	12	17	60	58	32
1.0	35	4	6	11	9	14	63	63	45
2.0	36	5	7	–	7	11	–	–	48
17.0	–	22	–	–	5	–	–	75	–

ERT enzyme replacement therapy, GSD II Glycogen storage disease type II, P patient no
^apatient died after abandoning treatment; — untreated

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