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Fig. 1 | Italian Journal of Pediatrics

Fig. 1

From: Severe congenital RYR1-associated myopathy complicated with atrial tachycardia and sinus node dysfunction: a case report

Fig. 1

ac Skeletal muscle (thyrohyoid muscle) histopathology was consistent with centronuclear myopathy. d and e Holter monitoring demonstrates sinus pause and junctional rhythms, confirming the diagnosis of sinus node dysfunction. a, hematoxylin & eosin; b, NADH-TR; c, modified Gomori-trichrome; calibration bar 20 μm; NADH-TR, nicotinamide adenine dinucleotide dehydrogenase - tetrazolium reductase.

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