Patients | Baseline | During NIV | After 1 year | P value |
---|---|---|---|---|
Age (years) | 23.8±6.0 |  |  |  |
LCI | 17.4±3.1 |  | 15.5±2.7 | <0.05 |
FEV1 % | 41.3±12 |  | 39.9±2.1 | ns |
PaO2 (mmHg) | 75.5±12 |  | 73.2±11 | ns |
PaCO2 (mmHg) | 41.8.±2.2 |  | 39.0.±2.1 | ns |
Awake SpO2 (%) | 96±0.8 |  | 96±0.4 | ns |
Awake respiratory rate | 21.7±2.2 |  | 23.2±1.8 | ns |
Exacerbations/year | 4.7±1.1 |  | 2.2±0.5 | <0.001 |
PG Parameters | Â | Â | Â | Â |
Meannocturnal SpO2 (%) | 91±1.0 | 94±1.0 |  | <0.001 |
Time with SpO2<90% | 9.1±3.2 | 3.4±1.7 |  | <0.01 |
Mean TcCO2 (mmHg) | 38.1±2.3 | 39.1±2.3 |  | ns |
AHI | 0.6±0.4 | 0.5±0.4 |  | ns |
Mean nocturnal RR | 28.4±4.2 | 23.5±1.9 |  | <0.01 |