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Table 2 Blood Transfusion and Chelation Therapy Data of the Study Population

From: CMV, B and C hepatitis among multi-transfused hereditary hemolytic Anemia children: an updated Egyptian experience

Transfusion and Chelation Variables

Data

Disease duration (years)

 - Mean (SD)

8.1 (±4.9)

 - Range

1–17

Age at 1st blood transfusion (years)

 - Mean (SD)

1.5 (±1.5)

 - Range

0.5–9

Blood transfusion duration (years)

 - Mean (SD)

8.04 (±4.94)

 - Range

1–17

RBC Transfusion Index (ml/kg/year)

 - Mean (SD)

183.14 (±48.5)

 - Range

30–360

Transfusion frequency (times/year)

 - Mean (SD)

12 (±6)

 - Range

4–20

Type of chelation No (%)

 - Deferasirox

204 (42.8)

 - Deferiprone

93 (19.5)

 - Desferoxamin

58 (12.2)

 - Combination) Deferasirox/Desferoxamine(

72 (15.1)

 - None

50 (10.5)

Compliance No (%)

 - Compliant

149 (35)

 -Noncompliant

278 (65)

Chelation duration (years)

 - Mean (SD)

7.2 (±4.6)

 - Range

0.5–17

  1. RBC’s Red Blood Cells, No Number, SD standard deviation