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Table 1 Anthropometric measures and evaluated indices of body composition before and during LAOS

From: L-alanine supplementation in Pompe disease (IOPD): a potential therapeutic implementation for patients on ERT? A case report

 

T0

T1

T2

Weight (kg)

28,3

29,4

30,5

Weight z-score (SD) §

0,36

0,15

0,17

Height (cm)

137,2

139,7

141,4

Height z-score(SD) §

1,27

1,03

1,03

BMI (kg/m2)

15,0

15,1

15,2

BMI z-score (SD)§

-0,49

-0,62

-0,58

FM %

9,9

11,6

13,4

FFM%

90,1

88,4

86,6

FM Kg

2,8

3,4

4,1

FFM Kg

25,5

26,0

26,4

  1. T0: baseline pre-LAOS; T1: after 6 months of LAOS start at 15 g/day; T2: after 3 months of increasing LAOS dosage (18 g/day) for a total of 9 months supplementation. Notes: § WHO 2007 Growth Charts
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Italian Journal of Pediatrics

ISSN: 1824-7288

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