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Table 1 Anthropometric measures and evaluated indices of body composition before and during LAOS

From: L-alanine supplementation in Pompe disease (IOPD): a potential therapeutic implementation for patients on ERT? A case report

  T0 T1 T2
Weight (kg) 28,3 29,4 30,5
Weight z-score (SD) § 0,36 0,15 0,17
Height (cm) 137,2 139,7 141,4
Height z-score(SD) § 1,27 1,03 1,03
BMI (kg/m2) 15,0 15,1 15,2
BMI z-score (SD)§ -0,49 -0,62 -0,58
FM % 9,9 11,6 13,4
FFM% 90,1 88,4 86,6
FM Kg 2,8 3,4 4,1
FFM Kg 25,5 26,0 26,4
  1. T0: baseline pre-LAOS; T1: after 6 months of LAOS start at 15 g/day; T2: after 3 months of increasing LAOS dosage (18 g/day) for a total of 9 months supplementation. Notes: § WHO 2007 Growth Charts