Skip to main content

Table 1 EB patients followed in Bambino Gesù Children’s Hospital 1990–2020

From: Multidisciplinary care for patients with epidermolysis bullosa from birth to adolescence: experience of one Italian reference center

N On follow-up Died/cause Lost to follow up Occasionally transited
All patients 215 140 (65%) 27 (13%) 11 (5%) 37 (17%)
DEBa 138 (64%) 97 (45%) 9 (5%) (RDEBb/SCCc) 9 (4%) 23 (11%)
JEB 30 (14%) 9 (4%) 18 (8%) (JEB-seve/sepsis) 2 (1%) 1 (0.5%)
EBSf 45 (21%) 32 (15%) 0 0 13 (6%)
KEBg 2 (1%) 2 (1%) 0 0 0
  1. aDEB, Dystrophic epidermolysis bullosa; bRDEB, Recessive DEB; cSCC, Squamous cell carcinoma, dJEB, junctional EB, eeJEB-sev, JEB severe, fEBS, EB simplex, gKEB, Kindler EB