Non-syndromic bile duct paucity and non-IgE cow’s milk allergy: a case report of challenging nutritional management and maltodextrin intolerance

Table 1 Summary of reported cases series of NSPBD

Publications		N	Prematurity	Age, mo	Sex	Jaundice	Pale stool	Hepatomegaly	Splenomegaly	Growth failure	Poor outcome
Bruguera et al., 1992 [8]		4	0/4	5—144	F > M	2/4	not reported	4/4	2/4	not reported	1 D 1 C
Chiu et al., 1996 [9]		4	not reported	0—132	M > F	4/4	not reported	4/4	2/4	4/4	3 D
Koçak et al., 1997 [10]		10	1/10	0.5 – 36	M > F	10/10	7/10	8/10	7/10	5/10	3 D
Yehezkely-Schildkraut et al., 2003 [11]		10	2/8	0 – 6	M > F	10/10	4/10	5/10	not reported	not reported	2 LF 4 UC
De Tommaso et al., 2004 [12]		11	2/11	1 – 40	M > F	11/11	8/11	6/11	4/11	1/11	1/11 C + LT
Meena et al., 2018 [3]	Non-destructive PILBD	20	7/20	4 – 12	M > F	18/20	10/20	20/20	19/20	11/20	3 LT
Meena et al., 2018 [3]	Destructive PILBD	50	8/50	4 – 97	M > F	48/50	23/50	49/50	47/50	22/50	26 LT
Mohanty et al., 2019 [13]		18	1/18	1 – 11	M > F	3/18	12/18	2/18	7/18	50–90%	1 D

N Number of patiens, Mo Months, M Male, F Female, D Death, LF Liver failure, R Renal disease, U Unchanged cholestasis, C Cirrhosis, LT Liver transplantation

ISSN: 1824-7288