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Table 1 The Neurocristopathies Classification

From: Multiple endocrine neoplasias type 2B and RET proto-oncogene

Simple neurocristopathies Complex Neurocristopathies
Non Neoplastic-Dysgenetic Neoplastic and Non-Neoplastic
   - Hirschsprung's disease    - Neurofibromatosis (Von Recklinghausen disease)
   - Albinism    - Multiple endocrine neoplasia (MEN) type 1
   - Mandibulofacial dysostosis    - MEN2A
   - Otocephaly    - MEN2B
   - Congenital Central Hypoventilation    - Neurocutaneous melanosis
   - Syndrome    - Familial neuroblastoma with Hirschprung' s disease
Neoplastic    - CCHS + HSCR = Haddad syndrome
   - Neuroblastoma    - Waardenburg + HSCR = Shah Waardenburg Syndrome
   - Pheochromocytoma  
   - Medullary thyroid carcinoma (MTC only)  
   - Noncromaffin paraganglioma  
   - Carcinoid tumors