Skip to main content

Table 5 MPS and tracheotomy

From: ENT and mucopolysaccharidoses

 

No. of patients

MPS type (n)

Tracheotomy (%)

Muhlebach, 2013 [37]

31

MPS I (9)

MPS II (19)

MPS III (1)

MPS IV (1)

MPS VI (1)

19.35%

Mesolella, 2013 [2]

20

MPS I (7)

MPS II (6)

MPS III (4)

MPS IV (1)

MPS VI (2)

5%

Malik, 2013 [19]

10

MPS II

100%

Complications:

Granulation (40%)

Wound infection (30%)

Ulceration (10%)

John, 2011 [12]

28

MPS VI

3.6%

Mendelsohn, 2010 [7]

527

MPS II

4.4%

Yeung, 2009 [29]

27

MPS IH (8)

MPS IH/S (3)

MPS II (5)

MPS III B (1)

MPS VI (1)

11%

Jeong, 2006 [46]

3

MPS II

100%

Complications:

Stomal narrowing (71.4%)

Granulation (57.1%)

Wound infection (28.6%)

Infrastomal stenosis (85.7%)

Bredenkamp, 1992 [38]

45

MPS IH (13)

MPS II (7)

MPS III (12)

MPS IV (6)

MPS VI (5)

MPS VII (2)

16%

  1. MPS mucopolysaccharidosis