| No. of patients | MPS type (n) | Tracheotomy (%) |
---|---|---|---|
Muhlebach, 2013 [37] | 31 | MPS I (9) MPS II (19) MPS III (1) MPS IV (1) MPS VI (1) | 19.35% |
Mesolella, 2013 [2] | 20 | MPS I (7) MPS II (6) MPS III (4) MPS IV (1) MPS VI (2) | 5% |
Malik, 2013 [19] | 10 | MPS II | 100% Complications: Granulation (40%) Wound infection (30%) Ulceration (10%) |
John, 2011 [12] | 28 | MPS VI | 3.6% |
Mendelsohn, 2010 [7] | 527 | MPS II | 4.4% |
Yeung, 2009 [29] | 27 | MPS IH (8) MPS IH/S (3) MPS II (5) MPS III B (1) MPS VI (1) | 11% |
Jeong, 2006 [46] | 3 | MPS II | 100% Complications: Stomal narrowing (71.4%) Granulation (57.1%) Wound infection (28.6%) Infrastomal stenosis (85.7%) |
Bredenkamp, 1992 [38] | 45 | MPS IH (13) MPS II (7) MPS III (12) MPS IV (6) MPS VI (5) MPS VII (2) | 16% |