From: FMF is not always “fever”: from clinical presentation to “treat to target”
Major criteria | |
1) Recurrent febrile episodes accompanied by peritonitis, synovitis, pleurisy | |
2) AA amyloidosis without a predisposing disease | |
3) Response to continuous colchicine administration | |
Minor criteria | |
1) Recurrent febrile episodes | |
2) Erysipelas-like erythema | |
3) FMF diagnosed in a first-degree relative |