| Number of patients | Males (%) | Females (%) | Age range (years) | Median age (years) | Mean age (years) | Patients < 1 year included (yes/no) | Minimum n. of patients < 1 y (available datab) | Maximum n. of patients < 1 y (available datab) | Number of patients < 1 year |
---|---|---|---|---|---|---|---|---|---|---|
Total | 1663 | 908 (54.6%) | 755 (45.4%) | 0 to 24 | Â | 4.2a | Â | 5/1663 (0.3%) | 41/1663 (2.4%) | 5 to 41 out of 1663 (0.3 to 2.4%) |
Connolly AM et al. 1994 [9] | 73 | 41 (56.2%) | 32 (43.8%) | 1 to 21 | N.A.a | 5.37 | No | / | / | / |
Evald L. et al. 2020I [26} | 3 | 2 (66.6%) | 1 (33.4%) | 3 to 15 | 4.3 | 4.6 | No | / | / | / |
GarcÃa-Iñiguez et al. 2019 [27] | 9 | 5 (55.5%) | 4 (44.5%) | 3 to 12 | 6.5 | 7.6 | No | / | / | / |
Garone G. et al. 2019 [6] | 509 | 273 (53.6%) | 236 (46.4%) | 1 to 18 | 4.4 | 5.8 | No | / | / | / |
Gieron-Korthals et al. 1994 [28} | 40 | 14 (35%) | 26 (65%) | 0 to 18 | N.A | 6.6 | Yes | 1 | 24 | Not specified |
Harai T. et al. 2010I [29] | 1 | 1 (100%) | 0 (0%) | 7 | 7 | 7 | No | / | / | / |
Hata A. et al. 2008 [30] | 2 | 1 (50%) | 1 (50%) | 1.3 | 1.3 | 1.3 | No | / | / | / |
Hennes E. et al. 2012 [31] | 11 | 6 (54.5%) | 5 (45.5%) | 3 to 14 | 6.7 | 6.9 | No | / | / | / |
Kirik S. et al. 2021 [5] | 39 | 21 (53.8%) | 18 (46.2%) | 1.5 to 16 | N.A | 6.2 | No | / | / | / |
Kornreich L. et al. 2016 [32] | 9 | 5 (55.5%) | 4 (44.5%) | 3 to 13 | 5.8 | 6.8 | No | / | / | / |
Lancella L. et al. 2017 [33] | 124 | 74 (59.7%) | 50 (40.3%) | 1 to 18 | N.A | 5.3 | No | / | / | / |
Luetje M. et al. 2019 [34] | 141 | 79 (56%) | 62 (44%) | 15Â months to 18Â years | N.A | 5.3 | No | / | / | / |
MartÃnez-G M. et al. 2006 [35] | 39 | 23 (59%) | 16 (41%) | 1.5 to 5 | N.A | 4.3 | No | / | / | / |
Muthusamy K. et al. 2019 [36] | 22 | 10 (45.4%) | 12 (54.6%) | 10Â months to 3.1Â years | N.A | 1.75 | Yes | 1 | 14 | Not specified |
Nussinovitch M. et al. 2003 [37] | 39 | 21 (53.8%) | 18 (46.2%) | 1 to 24 | N.A | 4.8 | No | / | / | / |
Rudloe T. et al. 2015 [38] | 364 | 196 (53.8%) | 168 (46.2%) | 1.7 to 5.5 | 2.8 | N.A | No | / | / | / |
Segal E. et al. 2019 [39] | 58 | 35 (60.3%) | 23 (39.7%) | 1 to 14 | N.A | 4.9 | No | / | / | / |
Thakkar K. et al. 2016 [7] | 120 | 66 (55%) | 54 (45%) | 6Â months to 18Â years | N.A | 4.5 | Yes | 3 | 3 | 3 |
Van der Maas et al. 2009 [14] | 45 | 25 (55.5%) | 20 (44.5%) | 1.4 to 12.9 | 2.8 | 3.7 | No | / | / | / |
Yildirim M. et al. 2020 [15] | 15 | 10 (66.6%) | 5 (33.4%) | 3 to 15 | 9.5 | 9.1 | No | / | / | / |